Te mohio ki nga tohu o te PML me te hunga o te reanga MS
Ko te leukoencephalopathy multifocal progressive (PML), ko te mate pukupuku kaore i mate i te mate a te JC . Ko tenei huaketo e mauhia ana i te takiwa e to rorohiko kaore e taea te kino.
Engari, mehemea ka ngoikore te puna o te mate taahua ki te mate, penei i te HIV / AIDS , te kanuiu , lymphoma, tetahi atu mate pukupuku, kaore ranei i pangia e te rongoā, ka rereketo te huaketo me te kino i to roro.
Ko te mate roro ka tukuna e PML ka arahina ki te maha o nga tohu.
Ahakoa he mea tino nui te PML, he nui atu te raruraru ki te whai koe i te sclerosis maha (MS) no te mea he mea whakamahara te rongoā o te mate ki te mate i te mate kia whakawhanakehia te PML.
Ko te Tysabri (natalizumab) e kitea ana he raruraru nui mo PML. Heoi ano, ko etahi atu rongoora MS kaore he matemate, tae atu ko Gilenya (fingolimod), Tecfidera (dimethyl fumarate), Ocrevus (ocrelizumab), me etahi atu.
Nga tohu tohu PML
Ko te MS e kore e whakanui ake i to tupono mo te PML. Engari, ki te mea ko koe, ko tetahi tangata e aroha ana, kei te tango i te rongoā mate-mate e whakakore ana i te pūnaha matehurai, e mohio ana koe ki nga tohu o te PML ka taea e koe te whakatikatika me te whakamohio i te aroturuki mo tenei raruraru kaha.
Ka rite ki nga tohu a MS, ko etahi e whai ana ki te PML rereke, i runga i te rohe o te roro.
Kei roto i nga tohu:
- He ngoikore, he maha i tetahi taha o te tinana
- Ko te kaha o te whakaaro hinengaro, e whakaatu pinepine ana he raruraru me te ngaro o te mahara
- He korero uaua
- Te ngoikoretanga o te mahi, te nuinga o te ahuatanga o te raruraru me te raruraru haere
- Nga raruraru o te tirohanga, penei i te kitenga matakite ranei, i te kore e kite marama i roto i tetahi waahanga motuhake o to taahi ataata
- Te rerekētanga o te tangata
- Nga mamae kino me te ngaro o te whakaaro i roto i te rohe o to tinana
- Nga pupuhi, ahakoa he iti noa tenei
PML vs. MS Relapse
Ko nga tohu o te PML he maha tonu nga mea e kore e kitea mai i etahi o te reanga MS. Ehara tenei i te mea miharo na te mea he mate whakaheke te mate o nga mate e rua, te tikanga o te whakangaromanga o te taonga tiaki i nga taana. Ko te ngaro o tenei taonga tiaki, e kiia nei ko te myelin, ka whakakore i te tuku o nga tohu hiko i waenga i to roro me te tinana.
No te mea ko nga tohu o te PML me te reanga MS ka taea te ahua tata, he mea uaua ki te tautuhi i te PML i nga wa o te mate. E ai ki tera, ko te tere o te whakawhanaketanga o nga tohu hou ko te tohu e awhina ana i te wehewehe mehemea e tika ana ki te PML me te reanga MS. Ko nga tohu o te PML kaore e puta wawe, engari ka whakawhanake me te ahu whakamua i nga ra ki nga wiki.
Ka taea e nga taakuta te rereke rereke i te PML mai i te MS ma te aromatawai tika i nga tohu a te tangata. No te mea he mate nui te PML o te roro, he maha atu i te kotahi o te tohu hou, ko te tohu kino ranei, ahakoa ko te ahuatanga o taua tohu ka kaha ake ki te hokinga mai o te MS. Heoi, he tohu noa tenei, ehara i te mea pakeke-a-tere.
Ko tetahi atu huarahi matua ki te wehe i te PML mai i te reanga MS ka tirotiro i te MRI ka tirotiro i te roro o te tangata.
Ka rite ki a MS, PML te mate pukupuku o te roro i runga i te MRI, engari ka rere ke atu i nga mate a MS me te rahi, te ahua, te waahi, me etahi atu momo.
Ka whakamahia te taatai ki te whakamatautau i te waipiro mo te huaketo JC hei whakauru i te waahanga o te PML. Ko te mutunga, ko te koiora roro kei te mahi i etahi wa.
He Kupu Mai i
E mohio ana mätou ko te hiahia pea o te whakawhanake i te PML he tino raruraru ina ka tango koe i etahi rongoā mate mate MS. Mena kei runga koe i Tysabri, Gilenya, Tecfidera, Ocrevus, ranei tetahi atu rongoa rongoā mo te MS, me te kite i tetahi tohu hou ranei, whakapiri atu ki to taote.
Ahakoa e kore e tohu enei tohu i te whakawhanaketanga o te PML, he tika tonu te aromatawai hauora, no te mea ko te mate pukupuku o te mate ko te whakawehi i te ora. Ko te toronga wawe ka hoatu ki a koe te painga pai mo te hua pai me whakawhanake koe i te PML.
> Mahinga:
> Bloomgren G, Richman S, Hotermans C, et al. Risk o Natalizumab-Associated Progressive Multifocal Leukoencephalopathy. N Engl J Med . 2012 Mei 17; 366 (20): 1870-80.
> Greenlee JE. Ko te Leukoencephalopathy (PML). I roto i: Porter RS, Kaplan JL, Lynn RB, et al. Merck Manual Professional Version .
> Maas RPPWM, Muller-Hansma AHG, Esselink RAJ, et al. Ko te Leukoencephalopathy Mahake-Whakakotahi Korero-He Korero: He Ngahau Hinengaro, Rongohau, me te Cerebrospinal Fluid Analysis of 326 Cases. J Neurol . 2016; 263 (10): 2004-2021.
> Te Whakahaere mo te Raa Rawa. (2015). Te Korero Maharo o te Leukoencephalopathy.
> Wollebo HS, White MK, Gordon J, Berger JR, Khalili K. Paaho me Pathogenesis o te Neurotropic Polyomavirus JC. Ann Neurol . 2015 Apr; 77 (4): 560-570.