Papatupuku Hinengaro Hinengaro

Ngā Kōwhiringa Whakamātautau

Mena ka mahue i te kaore, ka pangia te tinana e te cystic fibrosis (CF). Ka kitea te CF i mua, ka taea te maimoatanga wawe ki te aukati i te kino me te whakaiti i te haere tonu o te mate. I nga wa o mua, kua mate te mate o te tangata mai i te cystic fibrosis i mua i te wa e taea ai te mahi mate. I roto i nga tau kua pahure ake nei, kua whakawhanakehia nga whakamatautau e whakaaetia ai te taatai ​​i mua i te puta o te tohu tuatahi.

Te whakamātautau ira

Ko te whakamatautau taiao ko te huarahi anake hei korero mehemea kei te kawe te tangata i te ahua o te kirikarohi o te cystic fibrosis. Kei te mahi hoki i etahi wa kia kitea ai he tangata he cystic fibrosis, ko te tautuhi i nga whakawhitinga he tangata kei a CF.

Whakamātautau Prenatal

Ka taea te whakamatautau i nga momo taangata hei whakatau mehemea ka whanau mai he potae ki te fibrosis cystic. Mena ka mohio nga tokorua kua tatari kei te kawe i te ira kino, ka hiahia pea ratou ki te whakamatautau hei awhina ia ratou mehemea kaore i te whakamutu i te hapu. Mena ka whakaarohia e te tokorua te haere tonu o te whanau, ka mohiotia te waahi o te CF i mua i te whanau, a ka whai hua te pire ki te whiwhi wawe maimoatanga.

E rua nga whakamatautau ka taea te mahi i roto i te wa waahi. Ko nga whakamatautau e rua e tino kino ana, e kawe ana i te iti o te raruraru e tika ana kia whakawhitiwhitihia me te rata i mua i te whakamatautau.

Chorionic Villus Sampling (CVS): Ka tangohia te nui o te kikokiko mai i te raina me te tukuna ki te taiwhanga ki te whakatau mehemea kei te waahi te ira CFTR.

Kei te nuinga o tenei waa te whakamatautau i te wiki 11 o te hapu.

Amniocentesis: Kua nekehia te iti o te waikawa amniotic me te torongai me te serringe i roto i te kopu, ka tukuna ki te taiwhanga hei whakatau mehemea kei te waahi te ira CFTR. Kei te nuinga o te wa e mahi ana tenei whakamatautau i te wiki 16 o te hapu.

Whakaaturanga Hou

Kaore e taataihia e te whanau hou te CF, engari he hua pai e whakaara ake ana i te haki whero kia akiakihia te rata kia tono atu i etahi atu whakamatautau.

I roto i te United States, ko te nuinga o nga kaunihera kei te whakauru i nga whakamatautau o te cystic fibrosis i roto i ta ratau waahanga whakamatautau tamariki hou.

Te whakamātautau

Ko te whakamatautau wera ko te whakamatautau taatai ​​koura mo te CF mo etahi tau. Ko te whakamatautau wera he whakamatautau tere, kore-kore, he whakamatautau e kore e pai ki te whakarite i te taumata o te konutai me te waikawa i roto i te wera.Ko te tohu pai rawa o te fibrosis cystic engari kaore i te kuware.

Puna: Bilton, D (2008) .Cystic fibrosis. Tohu. 36, 273-278.