Ko te mate Neuroendocrine Pancreatic Cancer

He uiuinga me te Dr. Edward M. Wolin, MD

Ko te mate o Steve Jobs mai i te ahua o te mate pukupuku pancreatic e kiia nei ko te mate pukupuku neuroendocrine kua whakatairanga i te mate pukupuku pancreatic. I roto i tenei uiuinga, ko Dr. Edward Wolin, he tohunga mate pukupuku neuroendocrine e hono ana ki te Cedars Sinai Medical Center, e korero ana mo te mate pukupuku neuroendocrine pancreatic me pehea te pakanga o nga turoro. Ko Dr. Wolin te kaiwhakahaere-o te Carcinoid me te Neuroendocrine Tumor Program i te Cedars-Sinai Medical Center me tetahi o nga mahi tino nui o te motu e whakanui ana i te mate pukupuku neuroendocrine pancreatic.

Kihai ia i aro ki a Steve Jobs.

Ka taea e koe te whakamarama he aha te mate pukupuku neuroendocrine pancreatic?

Ko nga mate pukupuku neuroendocrine Pancreatic he pukupuku mate kino te tipu ka timata i nga ruma o te endocrin (nga pūtau whakaputa huatau) o te pancreas, he mea hoki e mohiotia ana ko nga ruma o te motu. Ahakoa ka taea e enei pukupuku te whakaputa i nga homoni pancreatics, kaore he tokomaha e whakaputa huamoni. He maha tonu nga horahanga e horahia ana ki roto i te taha pukupuku me te ate i te wa o te taatai. Engari, ko te tere o te oranga ka tino nui ake i te mate pukupuku o te pancreatic (adenocarcinoma) , ahakoa i te wa e noho ana nga tinana.

He aha te mea kua tohua? He tohu ranei?

Ina puta enei mate pukupuku i nga homoni, ka kaha te tohu o nga tohu o mua me te arahi ki te mahi wawe i te mate. Hei tauira, ko te tumuaki whakaputa-waihanga e whakaatu ana i nga tohu o te huka toto iti rawa , te pukupuku whakaputa-kawa ranei he nui te mate pukupuku me te mate duodenal, e arahina ana ki te whakamatau i te CT scan, MRI scan, or endoscopic ultrasound of the pancreas.

Mena kaore e hangaia e te hormone nga tohu haumanu, ka nui ake te tupu o te pukupuku ki te nui me te horapa ki te ate me etahi atu waahi i te wa e kitea ai i runga i te CT me te MRI. I roto i enei take, ko nga tohu tuatahi he mamae mamae, he tawhito, he mate taimaha, he ngoikore, he pupuhi i roto i te kopu, he ruaki, he pakarutanga kiri, he ngoikore, he mate pukupuku.

Ko wai kei te raru? Mehemea ko te toharite, kei te raruraru te tangata hauora mo te mate pukupuku neuroendocrine pancreatic?

He tino raruraru noa enei, me te mea he 3 take mo ia Amerika Amerika, kaute mo te 3% o nga mate pukupuku pancreatic. Na reira, ko te toharite, kaore te tangata hauora e whakaaro nui ki te whakawhanaketanga o te mate pukupuku neuroendocrine pancreatic. Ko te rereke kei etahi o nga hapu kei reira te mate pukupuku neuroendocrine pancreatic, he maha tonu te noho tahi me nga pukupuku parathyroid me te pituitary . Ko tenei waahitanga e mohiotia ana ko te momo neoplasia endocrine maha 1 (MEN-1).

Kei te mohio tatou he aha te take?

E mohio ana tatou he whakawhitinga - ko te ira ira tangata te MEN-1, a, e mohio ana tatou he maha ake nga rereketanga ira irakore i te mate pukupuku neuroendocrine, engari kaore i te mohiotia te take.

Kei te whai tetahi huarahi hei whakaiti i te painga, hei karo ranei i te mate pukupuku neuroendocrine pancreatic?

Kaore he huarahi mohio ki te whakaiti i te raruraru, ki te karo i te mate pukupuku neuroendocrine pancreatic.

He aha nga maimoatanga e wātea ana?

Na te mea he iti noa iho enei tumupuku i roto i te taupori whānui, me te momo tino atawhai o te tiaki, he kaha te whakatenatena o nga turoro ki te rapu korero mai i te pokapū tumuaki neuroendocrine. I roto i enei pokapū, he hononga tata ki te rongoā hauora , endocrinology, gastroenterology, pathology, pangiapera hepatobiliary, te taiao kano, te reo irirangi aukati, te reo radio diagnostic, me te rongoā karihi ki te arotau i te tiaki whaiaro o ia maimoatanga.

Ko nga maimoatanga ko te hanganga o nga tumuaki tuatahi me nga taatai, te whakakore i nga hanu me nga microwave, te rongoa i nga tumuaki me te rauropi rorohiko (radioembolization) me te chemotherapy (intrahepatic chememherapy), te whakanui i te tupuranga tumo me nga kaitohu koiora (nga analogo somatostatin, m-TOR, nga inhibitors tyrosine kinase , ko te rongoā radionuclide e kiia nei ko PRRT, te rongoā aukati, me te maimoatanga anti-angiogenic), me te whakamahi i te chemotherapy o- waha materoki -iti.

Hei ako atu mo Dr. Edward Wolin me tana mahi i Cedars Sinai Medical Center, tirohia te paetukutuku Cedars Sinai.